ZFIN is now using GRCz12tu for Genomic Data
Gene

rnf220b

ID
ZDB-GENE-081104-195
Name
ring finger protein 220b
Symbol
rnf220b Nomenclature History
Previous Names
  • si:ch211-241d21.7
Type
protein_coding_gene
Location
Chr: 8 Mapping Details/Browsers
Genome Assembly
GRCz12tu
Annotation Status
Current
Description
Human ortholog(s) of this gene implicated in hypomyelinating leukodystrophy 23. Orthologous to human RNF220 (ring finger protein 220).
Genome Resources
Note
None
Comparative Information
Expression
All Expression Data
No data available
Cross-Species Comparison
High Throughput Data
Thisse Expression Data
No data available
Wild Type Expression Summary
Phenotype
All Phenotype Data
No data available
Cross-Species Comparison
Alliance
Phenotype Summary
Mutations
Mutants
Sequence Targeting Reagents
Human Disease
Associated With rnf220b Human Ortholog
Disease Ontology Term Multi-Species Data OMIM Term OMIM Phenotype ID
hypomyelinating leukodystrophy 23 Alliance Leukodystrophy, hypomyelinating, 23, with ataxia, deafness, liver dysfunction, and dilated cardiomyopathy 619688
Associated With rnf220b Via Experimental Models
No data available
Gene Ontology
Protein Domains
Domain, Family, and Site Summary
Type InterPro ID Name
Domain IPR001841 Zinc finger, RING-type
Domain IPR031824 E3 ubiquitin-protein ligase RNF220, middle domain
Domain IPR040178 E3 ubiquitin-protein ligase RNF220, RING finger
Family IPR052443 E3 ubiquitin-protein ligase RNF220-like
Homologous_superfamily IPR013083 Zinc finger, RING/FYVE/PHD-type
Domain Details Per Protein
Protein Additional Resources Length E3 ubiquitin-protein ligase RNF220-like E3 ubiquitin-protein ligase RNF220, middle domain E3 ubiquitin-protein ligase RNF220, RING finger Zinc finger, RING/FYVE/PHD-type Zinc finger, RING-type
UniProtKB:A0A8N7TAR9 InterPro 588
UniProtKB:A0AC58G975 InterPro 656
UniProtKB:A0AC58G980 InterPro 684
UniProtKB:A0AC58G982 InterPro 656
UniProtKB:A0AC58G985 InterPro 649
UniProtKB:A0AC58G990 InterPro 621
UniProtKB:A0AC58G991 InterPro 621
UniProtKB:A0AC58G998 InterPro 656
UniProtKB:A0A8M6Z2A0 InterPro 553
Transcripts
Genome Browsers
Type Name Annotation Method Has Havana Data Length (nt) Analysis
mRNA rnf220-203 (1) Ensembl 1,903 nt
mRNA rnf220b-201 (1) Ensembl 1,108 nt
mRNA rnf220b-202 (1) Ensembl 3,450 nt
Interactions and Pathways
No data available
Antibodies
No data available
Plasmids
No data available
Constructs
Marker Relationships
Sequences
Genome Browsers
Orthology
Comparative Orthology
Alliance
Gene Tree
Ensembl
Citations