Term Name: prion disease
Synonyms: Prion disease pathway, prion induced disorder, Prion protein disease, Spongiform Encephalopathy, transmissible spongiform encephalopathy
Definition: A brain disease that is characterized by brain damage resulting from the abnormal folding, clumping and accumulation of cellular proteins in the brain induced by prion proteins.
Ontology: Human Disease [DOID:649]   ( DOID:649 )

Relationships
is a type of: brain disease disease by infectious agent
has subtype: chronic wasting disease Creutzfeldt-Jakob disease fatal familial insomnia Gerstmann-Straussler-Scheinker syndrome Huntington's disease-like 1 kuru scrapie variant Creutzfeldt-Jakob disease