| Term Name: | Gerstmann-Straussler-Scheinker syndrome |
|---|---|
| Synonyms: | Gerstmann-Straussler-Scheinker disease, PRION DEMENTIA |
| Definition: | A prion disease characterized by adult onset of memory loss, dementia, ataxia, and pathologic deposition of amyloid-like plaques in the brain. |
| Ontology: | Human Disease [DOID:4249] ( DOID:4249 ) |