Term Name:	isovaleric acidemia
Synonyms:	isovaleric acid CoA dehydrogenase deficiency, isovaleric aciduria, Isovaleryl-CoA dehydrogenase deficiency
Definition:	An organic acidemia that disrupts or prevents normal metabolism of the branched-chain amino acid leucine.
Ontology:	Human Disease [DOID:14753]   ( DOID:14753 )