Term Name: mutilating palmoplantar keratoderma with periorificial keratotic plaques
Synonyms: mutilating palmoplantar hyperkeratosis with periorificial keratotic plaques, OLMS, Olmsted syndrome, palmoplantar and periorificial keratoderma
Definition: A keratosis characterized by a bilateral mutilating palmoplantar keratoderma and periorificial keratotic plaques with severe pruritus of lesions.
Ontology: Human Disease [DOID:0112011]   ( DOID:0112011 )

Relationships
is a type of: keratosis
has subtype: autosomal dominant mutilating palmoplantar keratoderma with periorificial keratotic plaques X-linked mutilating palmoplantar keratoderma with periorificial keratotic plaques