Term Name: arrhythmogenic right ventricular cardiomyopathy
Synonyms: arrhythmogenic right ventricular dysplasia, arrhythmogenic right ventricular dysplasia/cardiomyopathy, ARVC, ARVC cardiomyopathy, ARVD, right ventricular ACM
Definition: An intrinsic cardiomyopathy that is characterized by hypokinetic areas involving the free wall of the right ventricle, with fibrofatty replacement of the right ventricular myocardium, with associated arrhythmias originating in the right ventricle and limited or no involvement of the left ventricle.
Ontology: Human Disease [DOID:0050431]   ( DOID:0050431 )

Relationships
is a type of: intrinsic cardiomyopathy
has subtype: arrhythmogenic right ventricular dysplasia 1 arrhythmogenic right ventricular dysplasia 3 arrhythmogenic right ventricular dysplasia 4 arrhythmogenic right ventricular dysplasia 5 arrhythmogenic right ventricular dysplasia 6 arrhythmogenic right ventricular dysplasia 8 arrhythmogenic right ventricular dysplasia 9 arrhythmogenic right ventricular dysplasia 10 arrhythmogenic right ventricular dysplasia 11 arrhythmogenic right ventricular dysplasia 12 arrhythmogenic right ventricular dysplasia 13 arrhythmogenic right ventricular dysplasia 14