Faller, K.M., Gutierrez-Quintana, R., Mohammed, A., Rahim, A.A., Tuxworth, R.I., Wager, K., Bond, M. (2015) The Neuronal Ceroid Lipofuscinoses: opportunities from model systems. Biochimica et biophysica acta. Molecular basis of disease. 1852(10 Pt B):2267-78
|
Mahmood, F., Fu, S., Cooke, J., Wilson, S.W., Cooper, J.D., and Russell, C. (2013) A zebrafish model of CLN2 disease is deficient in tripeptidyl peptidase 1 and displays progressive neurodegeneration accompanied by a reduction in proliferation. Brain : a journal of neurology. 136(Pt 5):1488-507
|